Anales de investigación clínica y de laboratorio

  • ISSN: 2386-5180
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Abstracto

A Case Study of Prune Belly Syndrome with Congenital Vesico-Subumbilical Skin Fistula

Allam Fayez Abuhamda and El-Sakka Mazen

Prune Belly Syndromes (PBS) usually fatal unless there is a communication between the fetal bladder and the amniotic sac. We report a case of PBS with congenital vesico-subumbilical skin fistula in a Palestinian male neonate. The patient had defect abdominal muscles, wrinkled abdominal skin, cryptorchidism, urethral atresia, vesico-subumbilical skin fistula and normal kidney function. Baby was discharged home in general condition with once daily prophylactic dose of oral amoxicillin. The baby needed multidisciplinary team approach for surgical repair in future, include; paediatric surgeon, paediatric urologist, paediatric nephrologists and paediatrician.